Available clinical studies demonstrate that triheptanoin directly addresses TCA cycle deficiencies that ... at diagnosis in mitochondrial fatty acid beta-oxidation defects: a French pediatric ...

When the body needs a lot of energy at a particular moment, the so-called beta oxidation is fired up - the fatty acids are "burned" straight away, so to speak. Medically, this metabolic pathway is ...

2015.06.006 7. Baruteau J, Sachs P, Broue P, et al. Clinical and biological features at diagnosis in mitochondrial fatty acid beta-oxidation defects: a French pediatric study of 187 patients.